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  Vol. 140 No. 2, February 2004 TABLE OF CONTENTS
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Multiple Eyelid Cysts With Palmoplantar Hyperkeratosis—Diagnosis

Arch Dermatol. 2004;140:231-236.

Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Diagnosis: Schopf-Schulz-Passarge syndrome.

MICROSCOPIC FINDINGS AND CLINICAL COURSE:

The biopsy specimen revealed large cystic spaces within the dermis. Two cell layers of the cystic wall were evident: outer cuboidal cells and inner columnar cells with decapitation secretion. These findings were consistent with multiple apocrine hidrocystomas. A diagnosis of Schopf-Schulz-Passarge syndrome was made. For skin cancer prophylaxis and possible treatment of both hyperkeratosis and apocrine hidrocystomas, acitretin therapy (25 mg/d) was initiated. There was minimal improvement of the hyperkertosis, and the acitretin therapy was discontinued.

DISCUSSION

In 1971, Schopf et al1 described the syndrome of multiple eyelid apocrine hidrocystomas, palmoplantar hyperkeratosis, hypodontia, and hypotrichosis. Since then, 20 cases (13 reports) have been reported in the literature.1-8 Multiple apocrine hidrocystomas of the eyelids have been described and can occur unrelated to this syndrome.

Schopf-Schulz-Passarge syndrome, which is characterized as a rare variant of ectodermal dysplasia,4 is commonly diagnosed in the second half of life.2 There are more than 150 recognized forms . . . [Full Text of this Article]


RELATED ARTICLE

Multiple Eyelid Cysts With Palmoplantar Hyperkeratosis—Quiz Case
Amy K. Gira, Dirk Robertson, and Robert A. Swerlick
Arch Dermatol. 2004;140(2):231-236.
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