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Jeremy P. Banky, MBBS; Adam T. Sheridan, FACD; Emma L. Storer, MBBS; Gillian Marshman, FACD
From the Churchill Hospital, Oxford Radcliffe Hospitals, Headington, Oxford, England (Drs Banky and Sheridan); and Flinders Medical Centre, Bedford Park, Australia (Drs Storer and Marshman).

Arch Dermatol. 2004;140:794-796.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

REPORT OF A CASE

A 53-year-old white woman with epidermolysis bullosa (EB) pruriginosa presented to the dermatology clinic seeking therapy for localized severe and intractable pruritus. At the age of 4 years the patient developed an extremely pruritic bullous eruption characterized by fragile blisters, erosions, and excoriations affecting sites subject to friction and pressure, particularly the ankles and knees. By the age of 21 years, the patient had large lichenified plaques, areas of linear violaceous scarring, multiple milia, and erosions over much of the extensor surfaces of the legs, forearms, buttocks, and dorsum of the feet (Figure 1A and B). All of her 20 nails were grossly dystrophic (Figure 1C). Mucous membranes were normal. There was a family history of EB pruriginosa, as the patient's younger brother and daughter were similarly affected.

Figure appears in full text version. Figure 1. Lichenified . . . [Full Text of this Article]

THERAPEUTIC CHALLENGE

SOLUTION

COMMENT



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