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Occurrence in a Patient With Ehlers-Danlos Syndrome Type IV

LCDR John Joseph Nanfro, MC

Arch Dermatol. 1982;118(9):695-696.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

Ehlers-Danlos type IV is characterized by joint hyperextensibility confined to the upper extremities, minimal skin hyperelasticity, and severe bleeding diatheses. Unlike the other types of Ehlers-Danlos syndrome, in type IV or the ecchymotic variety, the connective-tissue defect includes blood vessels, most often major arteries. A young man with this disorder was recently seen.

Report of a Case

A healthy 19-year-old man had large ecchymoses on his right arm while exercising on parallel bars. Because of the discomfort, he took 325 mg of aspirin every six hours. Two days later, while doing sit-ups, he noted acute, excruciating abdominal wall pain in the right hypogastrium. During the next 24 hours, a 10-cm ecchymotic area in the epigastrium developed, with a protuberant rectus sheath. The patient was referred to our hematology branch for examination the same day.

His history disclosed easy bruising since childhood. At age 6 years, he had a spontaneous rupture . . . [Full Text PDF of this Article]

Author Affiliations
USNR

From the Hematology-Oncology Branch, Department of Internal Medicine, and the Clinical Investigation Center, Naval Regional Medical Center, San Diego.

Footnotes
The opinions or assertions contained herein are those of the author and are not to be construed as official or as reflecting the views of the Navy Department of the Naval service at large.

Reprint requests to the Clinical Investigation Center, Naval Regional Medical Center, San Diego, CA 92134 (Dr Nanfro).

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