This Article  • References  • Full text PDF  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Citation map  • Citing articles on HighWire  • Citing articles on Web of Science (21)  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Social Bookmarking   What's this?

LOUIS RUBIN, M.D.; S. WILLIAM BECKER, Jr., M.D.

AMA Arch Derm. 1956;74(3):263-268.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

Some authors of recent articles on "incontinentia pigmenti" believe that Bloch-Sulzberger syndrome is a better name for this entity. The peculiar cutaneous hyper-pigmentation drew the attention of early investigators (Bardach,¹ Bloch,² Sulzberger,³ and Naegeli⁴) to this disease. The first impression of a pigmentary abnormality has been expanded until "incontinentia pigmenti" is now recognized to be a developmental defect showing many lesions of ectodermal and mesodermal origin (Curth,⁵ Epstein,⁶ Carney,⁷ Kitamura,⁸ Cramer,⁹ and Franceschetti¹⁰). Various lesions have been investigated histologically, but the origin and meaning of the pigment has never been explained.

We have been fortunate in being able to investigate this disease in two sisters

Report of Cases in Two Sisters

Family History.—Father is Irish, English, and French; mother is Mexican. Father had two normal children by previous wife. Mother was told by . . . [Full Text PDF of this Article]

Author Affiliations
Chicago

From the Department of Dermatology. University of Illinois College of Medicine; Marcus R. Caro, M.D., Head of the Department.

Footnotes
Accepted for publication Nov. 14, 1955.

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?