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Arch Dermatol. 1962;85(1):142-147.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

Tuberous Sclerosis. Presented by DR. W. B. REED.

A patient, age 55, is of normal mentality. The history is negative for epilepsy. Dermatological manifestations consist of (1) adenoma sebaceum since age 8 years; (2) shagreen patch of the lumbosacral area; (3) multiple ungual fibromas of hands and feet since "teen" age. Removal was followed by regrowth.

Roentgenogram of the skull was negative for calcification. On removal of a right ectopic kidney multiple hamartomas (angiomyolipomas) were found. The right eye has a phakoma. A bone survey showed "pagetoid changes;" fibrous displacement in pelvic bones, and cortical hyperostosis of phalanges.

The family history revealed that a sister, age 63, had ungual fibromas, but this was denied by the patient.

Past history of "rickets" and congenital dislocation of hips treated in childhood.

A patient, 4 years, has a history of slow mental development and 2 severe attacks of status epilepticus . . . [Full Text PDF of this Article]

Footnotes
Submitted for publication June 19, 1961.

Joint meeting.

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